Idiopathic pulmonary fibrosis (IPF) is a chronic disease of the lungs. It causes inflammation and scarring of lung tissue.
Idiopathic means the cause is not known.
Something starts uncontrolled inflammation. The inflammation damages tissue and leads to scarring. Over time, the scars surround the thin air sacs in the lungs. They make the sacs thicker and stiffer. Gases like oxygen will have a harder time passing through these sacs. You will have to breathe harder to get enough oxygen. The lungs will worsen until they lose their ability to pass oxygen.
Explore idiopathic pulmonary fibrosis. National Heart, Lung, and Blood Institute website. Available at: https://www.nhlbi.nih.gov/health-topics/idiopathic-pulmonary-fibrosis. Accessed January 17, 2019.
Idiopathic pulmonary fibrosis. American Thoracic Society. Available at: https://www.thoracic.org/patients/patient-resources/resources/idiopathic-pulmonary-fibrosis.pdf. Accessed January 17, 2019.
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