Single ventricle anomalies are rare heart conditions that can happen in a growing fetus. In a normal heart, the two ventricles work by collecting blood and pumping it to the lungs or the rest of the body. With this condition, one of the ventricles does not develop properly. The defect can be mild to severe. Other heart problems may also be present.
Examples of single ventricle anomalies are:
Tricuspid atresia—tricuspid valve does not develop
Pulmonary atresia—pulmonary valve does not develop
Hypoplastic left heart syndrome—left side of the heart does not develop properly
Double inlet left ventricle—large left ventricle and small right ventricle
Rao PS. Consensus on timing of intervention for common congenital heart diseases: part II - cyanotic heart defects. Indian J Pediatr. 2013 Aug;80(8):663-674.
Single ventricle anomalies and Fontan circulation. Cincinnati Children’s Hospital website. Available at: http://www.cincinnatichildrens.org/health/info/heart/diagnose/sv.htm. Accessed March 10, 2021.
Single ventricle defects. American Heart Association website. Available at: http://www.heart.org/HEARTORG/Conditions/CongenitalHeartDefects/AboutCongenitalHeartDefects/Single-Ventricle-Defects_UCM_307037_Article.jsp. Accessed March 10, 2021.
Single ventricle heart defects. Children’s Hospital of Philadelphia website. Available at: http://www.chop.edu/service/cardiac-center/heart-conditions/single-ventricle.html#treatment. Accessed March 10, 2021.
Tricuspid atresia. EBSCO DynaMed website. Available at: https://www.dynamed.com/condition/tricuspid-atresia. Accessed March 10, 2021.
Last reviewed December 2020 by
EBSCO Medical Review Board
Kari Kassir, MD
Last Updated: 3/10/2021
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