Pronounced: HIRSH-sprung ah–SO-shee-ay-ted ENT-ero-co-LYE-tis
Hirschsprung’s-associated enterocolitis (HAEC) is a complication of Hirschsprung’s disease. This is a rare condition that occurs in babies. It occurs when there are no nerve cells in the bowel. These nerve cells normally help control the bowel muscles that allow feces to move through the colon. The absence of these cells results in a bowel obstruction. This prevents normal bowel movements.
Enterocolitis is an inflammation or infection of the bowel. HAEC can happen suddenly and requires immediate care by a doctor. In most cases, hospital care is needed.
HAEC occurs when the bowel becomes inflamed or infected. This may be caused by:
Risk factors for HAEC include:
Symptoms may include:
These symptoms may be caused by other conditions. If your child has any of these symptoms, tell the doctor right away.
You will be asked about your child’s symptoms and medical history. A physical exam will be done.
Your child's bodily fluids may be tested. This can be done with blood tests.
Images may be taken of your child's bodily structures. This can be done with x-rays of the abdomen.
A child who has had pull-through surgery to treat an intestinal blockage will be closely monitored for symptoms of HAEC. While most cases of HAEC occur within 2 years after pull-through surgery, it can occur up to 10 years following surgery.
If the doctor suspects HAEC, barium enemas will be avoided. This is because of an increased risk of bowel perforation.
Talk with the doctor about the best treatment plan for your child. Treatment options include:
To help reduce your child’s chance of HAEC, rectal irrigation may be done after pull-through surgery to try to prevent HAEC.
American Academy of Pediatrics
International Foundation for Functional Gastrointestinal Disorders
Canadian Association of Gastroenterology
Canadian Paediatric Society
Hirschsprung’s Disease. About Kids GI website. Available at:
...(Click grey area to select URL)
Updated October 28, 2014. Updated October 30, 2014.
Kessmann J. Hirschsprung’s disease: diagnosis and management. Am Fam Physician. 2006 Oct 15;74(8):1319-1322.
Last reviewed December 2014 by Daus Mahnke, MD
Last Updated: 12/20/2014