CRDAMC Homepage | CRDAMC Library Phone #: (254) 288-8366 | CRDAMC Library Fax #: (254) 288-8368

Search Health Library

Port-Wine Stains

( Nevus flammeus )

Definition

A port-wine stain is a mark that is usually present at birth. It is made of enlarged blood vessels. This makes it appear as a reddish-purple patch of skin.

Causes    TOP

Port-wine stains are caused by a problem with the small blood vessels in the skin. Blood vessels can normally open and close to meet the needs of the skin. In port-wine stains, the blood vessels stay open. Blood fills the vessels causing the purple color and raised skin. This may be due to problems with the nerves controlling the blood vessels.

Risk Factors    TOP

There are no known risk factors for port-wine stains.

Conditions associated with port-wine stains include:

  • Sturge-Weber syndrome
  • Klippel-Trenaunay-Weber syndrome

Symptoms    TOP

The marks vary in size and are usually located on the head or neck, but may be in other locations

Appearance may change over time:

  • In children—they are flat, red, or light purple
  • In adults—they are raised and purplish in color, darkening and thickening over time

They may be prone to bleeding when scratched.

A port-wine stain near the eyes may be due to Sturge-Weber syndrome, and may cause additional symptoms

Diagnosis    TOP

A port-wine stain can typically be diagnosed based on its appearance. In some rare cases, a skin biopsy may be done. Other tests, such as eye examination or imaging, may be done if Sturge-Weber syndrome is suspected.

Skin Biopsy

Skin proceedure
Copyright © Nucleus Medical Media, Inc.

Treatment    TOP

Port-wine stains are generally harmless. They may occasionally result in dry skin, which may need moisturizing.

They may also cause emotional and social problems due to their visibility. Counseling may be considered.

Talk with your doctor about the best treatment plan for you. Treatment options include:

Lasers

Laser treatment may be used to destroy the blood vessels causing the stain. There are some risks with laser treatment. It may result in scarring and skin lightening or darkening.

Flash-lamp pumped pulse dye laser is one type used with port-wine stains. Multiple treatments may be necessary.

Other Treatments

Other treatment options include freezing, surgery, tattooing, and radiation. These treatments have had limited success. Lasers have replaced most of these treatments.

Prevention    TOP

There are no current guidelines to prevent port-wine stains.

RESOURCES:

American Academy of Dermatology
http://www.aad.org
Vascular Birthmarks Foundation
http://www.birthmark.org

CANADIAN RESOURCES:

Canadian Dermatology Association
http://www.dermatology.ca

References:

Port wine stain. Nemours Kids Health website. Available at:
...(Click grey area to select URL)
Updated September 2013. Accessed June 1, 2015.
Port-wine stain information. Vascular Birthmark Foundation website. Available at:
...(Click grey area to select URL)
Accessed June 1, 2016.
Alster TS, Tanzi EL. Combined 595-nm and 1,064-nm laser irradiation of recalcitrant and hypertrophic port-wine stains in children and adults. Dermatol Surg. 2009;35(6):914-918.
Jasim ZF, Handley JM. Treatment of pulsed dye laser-resistant port wine stain birthmarks. J Am Acad Dermatol. 2007;57(4):677-682.
Last reviewed June 2016 by Michael Woods, MD
Last Updated: 6/1/2016

EBSCO Information Services is fully accredited by URAC. URAC is an independent, nonprofit health care accrediting organization dedicated to promoting health care quality through accreditation, certification and commendation.

This content is reviewed regularly and is updated when new and relevant evidence is made available. This information is neither intended nor implied to be a substitute for professional medical advice. Always seek the advice of your physician or other qualified health provider prior to starting any new treatment or with questions regarding a medical condition.

To send comments or feedback to our Editorial Team regarding the content please email us at healthlibrarysupport@ebsco.com. Our Health Library Support team will respond to your email request within 2 business days.

Health Library: Editorial Policy | Privacy Policy | Terms and Conditions | Support
36000 Darnall Loop Fort Hood, Texas 76544-4752 | Phone: (254) 288-8000