Variant Creutzfeldt-Jakob disease (vCJD) is a type of prion disease that can cause death. Bovine spongiform encephalopathy (BSE) is a prion disease in cows. There is evidence that BSE can spread to humans. This results in vCJD. It is also known as mad cow disease.
It is believed that vCJD is caused by proteins called prions. Prions are normal proteins in the body. These prions may fold up in a way that is not normal. This can change them into the protein that causes the illness. The build up of these prions may be linked to from vCJD.
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Variant CJD is more common in younger people. Being around tissue that contains prions may raise your risk. This may happen from:
After you are exposed, it can take up to 20 years until you feel sick. Symptoms can follow these three phases:
Your doctor will ask about your symptoms and health history. A physical exam will be done. You may have:
Pictures may be taken with:
In many cases, a finding is not reached until an autopsy is done after death.
There is no cure for vCJD. You will receive support and help easing discomfort.
To lower your chance of getting vCJD, do not eat beef products. Avoid processed meat like sausages and hot dogs and beef items that contain brain, spinal cord, or bone marrow.
Creutzfeldt-Jakob Disease Foundation, Inc.
National Institute of Neurological Disorders and Stroke
Public Health Agency of Canada
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Last reviewed May 2018 by EBSCO Medical Review Board Rimas Lukas, MD Last Updated: 6/25/2018