Intestinal atresia (IA) is present at birth. It is an area of the intestine that has not formed the right way. In some, the intestine may be fully closed. Food or fluids can’t pass through.
IA can happen in the small or large intestines and may be named by where it is found:
It is not clear what causes IA. Low blood flow to the intestines before birth may play a role.
Some types of IA are due to genes. They tend to happen in people who are related.
If you are pregnant, you may raise your risk of having a child with IA if you:
IA may cause extra fluid to surround the baby during pregnancy.
Your baby may have:
A prenatal ultrasound will be able to detect extra fluid around the baby. The doctor may suspect the extra fluid is due to IA. More tests will be planned after birth to confirm the diagnosis.
After birth, your child’s doctor will review your child’s symptoms.
Pictures may be taken. This can be done with an abdominal X-ray
IA cannot be treated until after birth.
Surgery will be done to repair the intestine. Supportive care will be given.
Nutrition normally enters the body through the intestines. When the intestines are not working the right way, nutrition will be delivered into the blood stream. Your baby will have an IV or small belly button tube. Nutrition will be delivered through the tube before and after surgery.
After surgery, the intestines will need a few days or weeks to heal. Small amounts of breast milk or formula will be slowly introduced to your baby. IV nutrition will support your baby during this time. The IV will be removed when your baby can tolerate enough breast milk or formula.
Fluid and gas can build up in the intestine. They can cause swelling and vomiting. The fluid and gas can cause problems during surgery.
A tube will be passed through the nose and into the stomach. The tube will drain fluids and gas out of the stomach and intestines. This will ease some of the pressure in the abdomen.
Surgery will be needed to remove the damaged part of the intestine. The healthy parts will be reconnected. More steps may depend on the amount of intestine that is damaged. A large area may need more than one surgery.
A feeding tube may be placed through the abdomen. This tube will help drain the stomach and provide food.
Surgery in the lower intestine may also need a colostomy. The upper part of the intestine that is left is attached to an opening in the abdominal wall. This will allow waste to pass out of the body and give the lower intestines time to heal.
Most babies do well after surgery. Follow-up care will make sure that the intestines are working the right way.
IA can’t be prevented.
Centers for Disease Control and Prevention
Family Doctor—American Academy of Family Physicians
About Kids Health—The Hospital for Sick Children
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Last reviewed May 2018 by Kari Kassir, MD Last Updated: 7/2/2018